Sfoglia per Autore
Mouse sulphamidase gene: characterization of the promoter region of the gene and expression in mouse tissues
2003 Costanzi, Egidia; Beccari, Tommaso; Aisa, Maria Cristina; Tiribuzi, Roberto; Hopwood, J.; Orlacchio, Aldo
Phatophysiology studies improve the effectiveness of a therapeutic approach to Tay-Sachs disease
2004 Martino, Sabata; Tiribuzi, Roberto; Manieri, P.; Orlacchio, Aldo; Gritti, A.; Emiliani, Carla; Orlacchio, A.
Lysosomal glycoidrolases activities in dendritic cells: is it a function of hematopoietic stem cells differentiation process?
2004 Berardi, A. C.; Manieri, P.; Ciraci, E.; Tiribuzi, Roberto; DI GIROLAMO, Ilaria; Cavalieri, Cristina; Isacchi, G.; Emiliani, Carla; Bottazzo, G.; Orlacchio, Aldo; Martino, Sabata
Pathophysiology analysis improves the effectiveness of Tay-Sachs disease therapy
2004 Martino, Sabata; Tiribuzi, Roberto; Di Girolamo, I.; Manieri, P.; Gritti, A.; Emiliani, Carla; Orlacchio, Aldo
Alpha and Beta subunits of b-N-acethyl-hexosaminidase are differently regulated during the mammalian brain development: implication for Tay-Sachs disease therapy
2004 Martino, Sabata; Tiribuzi, Roberto; Di Girolamo, I.; Manieri, P.; Gritti, A.; Tancini, Brunella; Montanucci, Pia; Emiliani, Carla; Orlacchio, Aldo
Lysosomal glycohydrolases activities enhancement in dendritic cells is a function of hematopietic stem cells differentiation
2004 Martino, Sabata; Berardi, A.; Manieri, P.; Ciraci, E.; Tiribuzi, Roberto; Di Girolamo, I.; Cavalieri, C.; Ugazio, A.; Emiliani, Carla; Bottazzo, G.; Orlacchio, Aldo
Bone marrow stromal cells as a tool for gene/cell therapy for Tay-Sachs disease"
2004 Martino, Sabata; Tiribuzi, Roberto; Manieri, P.; Di Girolamo, I.; Emiliani, Carla; Orlacchio, Aldo
Bone marrow stromal cells as a tool for cell thepaty for lysosomal storage disorders with neurologic involvement
2005 Martino, Sabata; Tiribuzi, Roberto; Di Girolamo, I.; Orlacchio, Aldo; Emiliani, Carla; Orlacchio, Aldo
Expression and purification of a human, soluble Arylsulfatase A for Metachromatic Leukodystrophy enzyme replacement theraphy
2005 Martino, Sabata; Consiglio, A.; Cavalieri, Cristina; Tiribuzi, Roberto; Costanzi, Egidia; Severini, G. M.; Emiliani, Carla; Bordignon, C.; Orlacchio, Aldo
Cathepsin S, Cathepsin D and Cystatin C Balance: an immunomodulator molecular mechanism
2006 Tiribuzi, Roberto; Ciraci, E.; Di Girolamo, I.; D'Angelo, F.; Makrypidi, G.; Bottazzo, G.; Berardi, A.; Martino, Sabata; Orlacchio, Aldo
The Hex B gene is up-regulated during the brain development: effect for GM2 gangliosidosis therapy
2006 Martino, Sabata; Tiribuzi, Roberto; Di Girolamo, I.; Guadalupi, R.; D'Angelo, F.; Makrypidi, G.; Orlacchio, Aldo; Bernardi, G.; Orlacchio, A.
Beta-Hexosaminidase and immuno-response: implications for the neurodegenerative process in GM2 gangliosidosis
2006 Martino, Sabata; Tiribuzi, Roberto; Sonnino, S.; Chigorno, V.; Ciraci, E.; Berardi, A.; Orlacchio, Aldo
B-hexosaminidase isoenzymes and antigen presenting cell function: implication for neurodegenerative process in GM2-gangliosidosis
2006 Tiribuzi, Roberto; Ciraci, E.; Berardi, A.; Martino, Sabata; Orlacchio, Aldo
Hexosaminidase and brain development: improvement for GM2 gangliosidosis therapy
2006 Di Girolamo, I.; Tiribuzi, Roberto; Guadalupi, R.; D'Angelo, F.; Makrypidi, G.; Cavazzin, C.; Gritti, A.; Martino, Sabata; Orlacchio, Aldo
Generation of neural cells from bone marrow stromal-stem cells and human dental stem cells: a comparative study
2006 D'Angelo, F.; Tiribuzi, Roberto; Di Girolamo, I.; Makrypidi, G.; Laino, G.; Graziano, A.; Papaccio, G.; Martino, Sabata; Orlacchio, Aldo
Lysosomal aspartic protease cathepsin D processing as a novel biomarker for hematopietic stem cells
2007 Tiribuzi, Roberto; Berardi, A. C.; Martino, Sabata; Orlacchio, Aldo
Beta-Hexosaminidase expression is recapitulated in Neural Stem Cells induced to differentiate and in embryonic to adult brain development in both WT and knock-out mice
2007 Martino, Sabata; di Girolamo, I.; Tiribuzi, Roberto; Makrypidi, G.; D'Angelo, F.; Mattoli, F.; Cavazzin, C.; Galli, R.; Sandhoff, K.; Gritti, A.; Orlacchio, Aldo
Implication of Cathepsin S and D, and of the Lysosomal Cysteine Protease Inhibitor Cystatin C during TPO+IL-16-Induced Generation of Tolerogenic Dendritic Cells from Hematopoietic Stem Cells
2007 Martino, Sabata; Tiribuzi, Roberto; Makrypidi, G.; di Girolamo, I.; D'Angelo, F.; Ciraci, E.; Datti, Alessandro; Berardi, A. C.; Orlacchio, Aldo
Knockdown of HEX genes generate a tolerogenic-like dendritic cells phenotype
2007 Martino, Sabata; Tiribuzi, Roberto; di Girolamo, I.; Makrypidi, G.; D'Angelo, F.; Massini, C.; Ciraci, E.; Berardi, A. C.; Orlacchio, Aldo
Promoters characterization of the gene coding for mouse and bovine di-N-acetylchitobiase
2007 Balducci, C.; Persichetti, E.; Tiribuzi, Roberto; Codini, Michela; Martino, Sabata; Orlacchio, Aldo; Beccari, Tommaso
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
Mouse sulphamidase gene: characterization of the promoter region of the gene and expression in mouse tissues | 2003 | Costanzi, Egidia; Beccari, Tommaso; Aisa, Maria Cristina; Tiribuzi, Roberto; Hopwood, J.; Orlacchio, Aldo | |
Phatophysiology studies improve the effectiveness of a therapeutic approach to Tay-Sachs disease | 2004 | Martino, Sabata; Tiribuzi, Roberto; Manieri, P.; Orlacchio, Aldo; Gritti, A.; Emiliani, Carla; Orlacchio, A. | |
Lysosomal glycoidrolases activities in dendritic cells: is it a function of hematopoietic stem cells differentiation process? | 2004 | Berardi, A. C.; Manieri, P.; Ciraci, E.; Tiribuzi, Roberto; DI GIROLAMO, Ilaria; Cavalieri, Cristina; Isacchi, G.; Emiliani, Carla; Bottazzo, G.; Orlacchio, Aldo; Martino, Sabata | |
Pathophysiology analysis improves the effectiveness of Tay-Sachs disease therapy | 2004 | Martino, Sabata; Tiribuzi, Roberto; Di Girolamo, I.; Manieri, P.; Gritti, A.; Emiliani, Carla; Orlacchio, Aldo | |
Alpha and Beta subunits of b-N-acethyl-hexosaminidase are differently regulated during the mammalian brain development: implication for Tay-Sachs disease therapy | 2004 | Martino, Sabata; Tiribuzi, Roberto; Di Girolamo, I.; Manieri, P.; Gritti, A.; Tancini, Brunella; Montanucci, Pia; Emiliani, Carla; Orlacchio, Aldo | |
Lysosomal glycohydrolases activities enhancement in dendritic cells is a function of hematopietic stem cells differentiation | 2004 | Martino, Sabata; Berardi, A.; Manieri, P.; Ciraci, E.; Tiribuzi, Roberto; Di Girolamo, I.; Cavalieri, C.; Ugazio, A.; Emiliani, Carla; Bottazzo, G.; Orlacchio, Aldo | |
Bone marrow stromal cells as a tool for gene/cell therapy for Tay-Sachs disease" | 2004 | Martino, Sabata; Tiribuzi, Roberto; Manieri, P.; Di Girolamo, I.; Emiliani, Carla; Orlacchio, Aldo | |
Bone marrow stromal cells as a tool for cell thepaty for lysosomal storage disorders with neurologic involvement | 2005 | Martino, Sabata; Tiribuzi, Roberto; Di Girolamo, I.; Orlacchio, Aldo; Emiliani, Carla; Orlacchio, Aldo | |
Expression and purification of a human, soluble Arylsulfatase A for Metachromatic Leukodystrophy enzyme replacement theraphy | 2005 | Martino, Sabata; Consiglio, A.; Cavalieri, Cristina; Tiribuzi, Roberto; Costanzi, Egidia; Severini, G. M.; Emiliani, Carla; Bordignon, C.; Orlacchio, Aldo | |
Cathepsin S, Cathepsin D and Cystatin C Balance: an immunomodulator molecular mechanism | 2006 | Tiribuzi, Roberto; Ciraci, E.; Di Girolamo, I.; D'Angelo, F.; Makrypidi, G.; Bottazzo, G.; Berardi, A.; Martino, Sabata; Orlacchio, Aldo | |
The Hex B gene is up-regulated during the brain development: effect for GM2 gangliosidosis therapy | 2006 | Martino, Sabata; Tiribuzi, Roberto; Di Girolamo, I.; Guadalupi, R.; D'Angelo, F.; Makrypidi, G.; Orlacchio, Aldo; Bernardi, G.; Orlacchio, A. | |
Beta-Hexosaminidase and immuno-response: implications for the neurodegenerative process in GM2 gangliosidosis | 2006 | Martino, Sabata; Tiribuzi, Roberto; Sonnino, S.; Chigorno, V.; Ciraci, E.; Berardi, A.; Orlacchio, Aldo | |
B-hexosaminidase isoenzymes and antigen presenting cell function: implication for neurodegenerative process in GM2-gangliosidosis | 2006 | Tiribuzi, Roberto; Ciraci, E.; Berardi, A.; Martino, Sabata; Orlacchio, Aldo | |
Hexosaminidase and brain development: improvement for GM2 gangliosidosis therapy | 2006 | Di Girolamo, I.; Tiribuzi, Roberto; Guadalupi, R.; D'Angelo, F.; Makrypidi, G.; Cavazzin, C.; Gritti, A.; Martino, Sabata; Orlacchio, Aldo | |
Generation of neural cells from bone marrow stromal-stem cells and human dental stem cells: a comparative study | 2006 | D'Angelo, F.; Tiribuzi, Roberto; Di Girolamo, I.; Makrypidi, G.; Laino, G.; Graziano, A.; Papaccio, G.; Martino, Sabata; Orlacchio, Aldo | |
Lysosomal aspartic protease cathepsin D processing as a novel biomarker for hematopietic stem cells | 2007 | Tiribuzi, Roberto; Berardi, A. C.; Martino, Sabata; Orlacchio, Aldo | |
Beta-Hexosaminidase expression is recapitulated in Neural Stem Cells induced to differentiate and in embryonic to adult brain development in both WT and knock-out mice | 2007 | Martino, Sabata; di Girolamo, I.; Tiribuzi, Roberto; Makrypidi, G.; D'Angelo, F.; Mattoli, F.; Cavazzin, C.; Galli, R.; Sandhoff, K.; Gritti, A.; Orlacchio, Aldo | |
Implication of Cathepsin S and D, and of the Lysosomal Cysteine Protease Inhibitor Cystatin C during TPO+IL-16-Induced Generation of Tolerogenic Dendritic Cells from Hematopoietic Stem Cells | 2007 | Martino, Sabata; Tiribuzi, Roberto; Makrypidi, G.; di Girolamo, I.; D'Angelo, F.; Ciraci, E.; Datti, Alessandro; Berardi, A. C.; Orlacchio, Aldo | |
Knockdown of HEX genes generate a tolerogenic-like dendritic cells phenotype | 2007 | Martino, Sabata; Tiribuzi, Roberto; di Girolamo, I.; Makrypidi, G.; D'Angelo, F.; Massini, C.; Ciraci, E.; Berardi, A. C.; Orlacchio, Aldo | |
Promoters characterization of the gene coding for mouse and bovine di-N-acetylchitobiase | 2007 | Balducci, C.; Persichetti, E.; Tiribuzi, Roberto; Codini, Michela; Martino, Sabata; Orlacchio, Aldo; Beccari, Tommaso |
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